Computed tomographic findings in bourneville-pringle disease.
Dokumenttyp:
Case Reports; Journal Article; Article
Autor(en):
Beltle, J; Seemann, MD
Abstract:
Bourneville-Pringle disease (synonym: tuberous sclerosis, epiploia) is a neuroectodermal disorder. A characteristic clinical triad of adenoma sebaceum, mental retardartion, and seizures leads to early childhood diagnosis. Many patients show morphological changes of the visceral organs, vascular, and skeletal system. We review the computed tomographic findings of Bourneville-Pringle disease as relates to an oligosymptomatic 36-year-old woman with late onset of clinical symptoms.