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Document type:
journal article 
Author(s):
Anlauf, M; Garbrecht, N; Bauersfeld, J; Schmitt, A; Henopp, T; Komminoth, P; Heitz, PU; Perren, A; Klöppel, G 
Title:
Hereditary neuroendocrine tumors of the gastroenteropancreatic system. 
Abstract:
Approximately 5-10% of neuroendocrine tumors (NETs) of the gastroenteropancreatic system (GEP) have a hereditary background. The known inherited syndromes include multiple endocrine neoplasia type 1, neurofibromatosis type 1, von Hippel-Lindau disease, and the tuberous sclerosis complex. This review discusses for each of these syndromes the: (1) involved genes and specific types of mutations, (2) disease prevalence and penetrance, (3) affected neuroendocrine tissues and related clinical syndrome...    »
 
Journal title abbreviation:
Virchows Arch 
Year:
2007 
Journal volume:
451 Suppl 
Pages contribution:
S29-38 
Language:
eng 
Print-ISSN:
0945-6317 
TUM Institution:
r Allgemeine Pathologie und pathologische Anatomie